Kawasaki disease(KD)is an acute self-limited febrile systemic vasculitis of unknown cause and often occurs in children under 5 years old[1].Macrophage activation syndrome(MAS),also known as secondary hemophagocytic ly...Kawasaki disease(KD)is an acute self-limited febrile systemic vasculitis of unknown cause and often occurs in children under 5 years old[1].Macrophage activation syndrome(MAS),also known as secondary hemophagocytic lymphohistiocytosis(HLH),is a life-threatening complication associated with autoimmune and/or inflammatory disorders including KD[2].The incidence of MAS in pediatric patients with KD has been reported to range 1.1~1.9%[3,4].KD-MAS has never been reported in Macao.In this article,we presented the clinical features,laboratory characteristics,and treatment outcomes of a patient with KD complicated with MAS.展开更多
文摘Kawasaki disease(KD)is an acute self-limited febrile systemic vasculitis of unknown cause and often occurs in children under 5 years old[1].Macrophage activation syndrome(MAS),also known as secondary hemophagocytic lymphohistiocytosis(HLH),is a life-threatening complication associated with autoimmune and/or inflammatory disorders including KD[2].The incidence of MAS in pediatric patients with KD has been reported to range 1.1~1.9%[3,4].KD-MAS has never been reported in Macao.In this article,we presented the clinical features,laboratory characteristics,and treatment outcomes of a patient with KD complicated with MAS.
