Rationale:Herlyn-Werner-Wunderlich syndrome,also known as obstructed hemi-vagina with ipsilateral renal agenesis(OHVIRA)syndrome,is a rare congenital anomaly of the Müllerian and Wolffian ducts.It is often asympt...Rationale:Herlyn-Werner-Wunderlich syndrome,also known as obstructed hemi-vagina with ipsilateral renal agenesis(OHVIRA)syndrome,is a rare congenital anomaly of the Müllerian and Wolffian ducts.It is often asymptomatic until puberty and is usually misdiagnosed as infertility.Patient concerns:A 39-year-old woman desirous of pregnancy was referred to our radiodiagnosis unit for imaging evaluation on account of secondary infertility.Diagnosis:Incidental discovery of uterine bicornis bicollis and blind-ending hemivagina was noted at hysterosalpingography.Interventions:This necessitated the search for other genitourinary tract anomalies,and ipsilateral renal agenesis was also discovered.Outcomes:A diagnosis of Herlyn-Werner-Wunderlich syndrome was made.Lessons:Magnetic resonance imaging(MRI)is considered the gold standard imaging modality for the assessment of uterine malformations.However,in resource-poor centers where MRI is unavailable,a heightened clinical suspicion with the combination of available imaging modalities is important and reliable in making an accurate diagnosis,hence,successful management.展开更多
文摘Rationale:Herlyn-Werner-Wunderlich syndrome,also known as obstructed hemi-vagina with ipsilateral renal agenesis(OHVIRA)syndrome,is a rare congenital anomaly of the Müllerian and Wolffian ducts.It is often asymptomatic until puberty and is usually misdiagnosed as infertility.Patient concerns:A 39-year-old woman desirous of pregnancy was referred to our radiodiagnosis unit for imaging evaluation on account of secondary infertility.Diagnosis:Incidental discovery of uterine bicornis bicollis and blind-ending hemivagina was noted at hysterosalpingography.Interventions:This necessitated the search for other genitourinary tract anomalies,and ipsilateral renal agenesis was also discovered.Outcomes:A diagnosis of Herlyn-Werner-Wunderlich syndrome was made.Lessons:Magnetic resonance imaging(MRI)is considered the gold standard imaging modality for the assessment of uterine malformations.However,in resource-poor centers where MRI is unavailable,a heightened clinical suspicion with the combination of available imaging modalities is important and reliable in making an accurate diagnosis,hence,successful management.
