Hepatocellular adenoma(HCA)is one of the important complications of glycogen storage disease typeⅠa(GSD-Ⅰa)because it can be transformed into hepatocellular carcinoma.Although surgical resection is a standard treatm...Hepatocellular adenoma(HCA)is one of the important complications of glycogen storage disease typeⅠa(GSD-Ⅰa)because it can be transformed into hepatocellular carcinoma.Although surgical resection is a standard treatment of choice for solitary HCA,multiple HCAs in GSD-Ⅰa patients present as therapeutic challenges for curative treatment.Therefore,treatment strategy according to malignant potential is important in management of HCAs in GSD-Ⅰa.The authors present a case of histologically proven multiple HCAs withoutβ-catenin mutations occurred in a GSD-Ⅰa patient treated successfully with percutaneous radiofrequency ablation as a minimally invasive therapy.展开更多
文摘Hepatocellular adenoma(HCA)is one of the important complications of glycogen storage disease typeⅠa(GSD-Ⅰa)because it can be transformed into hepatocellular carcinoma.Although surgical resection is a standard treatment of choice for solitary HCA,multiple HCAs in GSD-Ⅰa patients present as therapeutic challenges for curative treatment.Therefore,treatment strategy according to malignant potential is important in management of HCAs in GSD-Ⅰa.The authors present a case of histologically proven multiple HCAs withoutβ-catenin mutations occurred in a GSD-Ⅰa patient treated successfully with percutaneous radiofrequency ablation as a minimally invasive therapy.
