Abernethy malformation （AM） is a rare congenital anomaly in which the splanchnic blood bypasses the liver and drains directly into the systemic veins.It was first described by Abemethy in 1793 and has two types.Type...Abernethy malformation （AM） is a rare congenital anomaly in which the splanchnic blood bypasses the liver and drains directly into the systemic veins.It was first described by Abemethy in 1793 and has two types.Type Ⅰ is characterized by a complete portosystemic shunt and an absence of a portal vein （consists of superior mesenteric and splenic veins）,while Type Ⅱ exhibits partial portosystemic shunt and a hypoplastic portal vein.Type Ⅰ is further subclassified into subtype a and b based on the absence or presence of a patent connection between the superior mesenteric vein and the splenic vein.展开更多
文摘Abernethy malformation （AM） is a rare congenital anomaly in which the splanchnic blood bypasses the liver and drains directly into the systemic veins.It was first described by Abemethy in 1793 and has two types.Type Ⅰ is characterized by a complete portosystemic shunt and an absence of a portal vein （consists of superior mesenteric and splenic veins）,while Type Ⅱ exhibits partial portosystemic shunt and a hypoplastic portal vein.Type Ⅰ is further subclassified into subtype a and b based on the absence or presence of a patent connection between the superior mesenteric vein and the splenic vein.
