BACKGROUND Purpura annularis telangiectodes of Majocchi(PATM),also known as Majocchi,is a rare subclass of pigmented purpuric dermatoses.The etiology of PATM is unknown,but it seems more common in children and young w...BACKGROUND Purpura annularis telangiectodes of Majocchi(PATM),also known as Majocchi,is a rare subclass of pigmented purpuric dermatoses.The etiology of PATM is unknown,but it seems more common in children and young women.The skin lesions are mostly symmetrical ring-shaped reddish-brown macules on the lower limbs.CASE SUMMARY A 9-year-old girl,who has received treated in our department,presented with reddish-brown ring-shaped rash on both lower limbs that had been present for 6 mo.These lesions,red brownish annular or petaloid patches,were mostly found on ankles and lower limber,which do not fade when adding pressure and no feel of infiltration and no atrophy when touching those lesions.Pathological examination showed deposition of hemosiderin in papillary dermis.However,dermoscopy showed the pigmentation in the center as well as the lavender patches on the edge of lesion.The child was thus diagnosed with PATM.After diagnosis,we suggested the patient avoid strenuous exercise.she was given vitamin C tablets for oral and mometasone furoate cream for external use.Followup examinations and treatment continue to support the clinical diagnosis to date.CONCLUSION This is the first report of investigating PATM using dermoscopy,which can differentiate PATM from other diseases due to its unique microscopic feature under dermoscopy.Although PATM is harmless,it still requires long-term follow-up.Moreover,dermoscopy technique can be applied for observation of multi-site lesions and correlated with histopathology.Thus,we believe this approach could be generalized for future diagnosis of PATM.展开更多
BACKGROUND Syringocystadenoma papilliferum(SCAP)represents a rare,noncancerous adnexal tumor predominantly presenting at birth or in early childhood.CASE SUMMARY In this study,a 35-day-old girl was admitted to Kunming...BACKGROUND Syringocystadenoma papilliferum(SCAP)represents a rare,noncancerous adnexal tumor predominantly presenting at birth or in early childhood.CASE SUMMARY In this study,a 35-day-old girl was admitted to Kunming Children’s Hospital in October 2019 due to a lesion in the right frontotemporal region since birth.The surface of the lesion was bright red,granular,and papillary and easily bled upon touch,with about 1.5 cm×4 cm in size.A subcutaneous mass was felt at the base of the lesion,with a size of about 3 cm×5 cm.Dermatoscopy showed that the skin lesion was lobular and crumby.The lesion center was reddish or white,while the edges were white or yellowish band-like.There were polymorphic vascular structures and white radial streaks in the lesion,with some vascular clusters scattered.Pathological examination showed papilloma-like hyperplasia of the epidermis,with the epidermis partly sinking into the dermis to form several cystic depressions.Combining clinical and histopathological features,the child was diagnosed with SCAP.Follow-up is ongoing,and surgical resection will be performed.CONCLUSION This was a special clinical manifestation of SCAP,which complements the clinical manifestations of the disease and provides new insights for the diagnosis and differentiation of neonatal skin tumors.展开更多
基金Supported by the Scientific Research Foundation of the Education Department of Yunnan Province,No.2023J0293。
文摘BACKGROUND Purpura annularis telangiectodes of Majocchi(PATM),also known as Majocchi,is a rare subclass of pigmented purpuric dermatoses.The etiology of PATM is unknown,but it seems more common in children and young women.The skin lesions are mostly symmetrical ring-shaped reddish-brown macules on the lower limbs.CASE SUMMARY A 9-year-old girl,who has received treated in our department,presented with reddish-brown ring-shaped rash on both lower limbs that had been present for 6 mo.These lesions,red brownish annular or petaloid patches,were mostly found on ankles and lower limber,which do not fade when adding pressure and no feel of infiltration and no atrophy when touching those lesions.Pathological examination showed deposition of hemosiderin in papillary dermis.However,dermoscopy showed the pigmentation in the center as well as the lavender patches on the edge of lesion.The child was thus diagnosed with PATM.After diagnosis,we suggested the patient avoid strenuous exercise.she was given vitamin C tablets for oral and mometasone furoate cream for external use.Followup examinations and treatment continue to support the clinical diagnosis to date.CONCLUSION This is the first report of investigating PATM using dermoscopy,which can differentiate PATM from other diseases due to its unique microscopic feature under dermoscopy.Although PATM is harmless,it still requires long-term follow-up.Moreover,dermoscopy technique can be applied for observation of multi-site lesions and correlated with histopathology.Thus,we believe this approach could be generalized for future diagnosis of PATM.
文摘BACKGROUND Syringocystadenoma papilliferum(SCAP)represents a rare,noncancerous adnexal tumor predominantly presenting at birth or in early childhood.CASE SUMMARY In this study,a 35-day-old girl was admitted to Kunming Children’s Hospital in October 2019 due to a lesion in the right frontotemporal region since birth.The surface of the lesion was bright red,granular,and papillary and easily bled upon touch,with about 1.5 cm×4 cm in size.A subcutaneous mass was felt at the base of the lesion,with a size of about 3 cm×5 cm.Dermatoscopy showed that the skin lesion was lobular and crumby.The lesion center was reddish or white,while the edges were white or yellowish band-like.There were polymorphic vascular structures and white radial streaks in the lesion,with some vascular clusters scattered.Pathological examination showed papilloma-like hyperplasia of the epidermis,with the epidermis partly sinking into the dermis to form several cystic depressions.Combining clinical and histopathological features,the child was diagnosed with SCAP.Follow-up is ongoing,and surgical resection will be performed.CONCLUSION This was a special clinical manifestation of SCAP,which complements the clinical manifestations of the disease and provides new insights for the diagnosis and differentiation of neonatal skin tumors.
