The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small a...The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small and symmetrical receded mandible), glossoptosis (tongue of variable size falls backwards into the post pharyngeal wall), and cleft palate (U or V shaped). We report a case of 2 hours old newborn presented with micrognathia, retrognathia, and glossoptosis and absent anterior two thirds of tongue.展开更多
Pierre Robin sequence(PRS)is a triad of micrognathia,glossoptosis,and cleft palate that results in an obstruction of the airway on inspiration and impeding feeding.The tongue of infants with PRS fall back toward the p...Pierre Robin sequence(PRS)is a triad of micrognathia,glossoptosis,and cleft palate that results in an obstruction of the airway on inspiration and impeding feeding.The tongue of infants with PRS fall back toward the posterior pharyngeal wall(glossoptosis)due to receding chin produced by mandibular micrognathia(small jaw)or retrognathia.This causes a serious condition with potentially severe,life-threatening airway obstruction.If untreated,this problem can lead to exhaustion,cardiac failure,and ultimately death,especially during the early months of life.Actually,in the majority of PRS infants,these symptoms can be managed by placing the infant in the prone position until adequate growth of the jaw occurs.If this type of treatment fails,the infant then should be considered for other conservative therapies or surgical interventions.This paper reviews surgical interventions such as tongue-lip adhesion,mandibular traction,mandibular distraction,tracheotomy and conservative orthodontic approaches,and presents a baby treated successfully with an orthodontic appliance.展开更多
文摘The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small and symmetrical receded mandible), glossoptosis (tongue of variable size falls backwards into the post pharyngeal wall), and cleft palate (U or V shaped). We report a case of 2 hours old newborn presented with micrognathia, retrognathia, and glossoptosis and absent anterior two thirds of tongue.
文摘Pierre Robin sequence(PRS)is a triad of micrognathia,glossoptosis,and cleft palate that results in an obstruction of the airway on inspiration and impeding feeding.The tongue of infants with PRS fall back toward the posterior pharyngeal wall(glossoptosis)due to receding chin produced by mandibular micrognathia(small jaw)or retrognathia.This causes a serious condition with potentially severe,life-threatening airway obstruction.If untreated,this problem can lead to exhaustion,cardiac failure,and ultimately death,especially during the early months of life.Actually,in the majority of PRS infants,these symptoms can be managed by placing the infant in the prone position until adequate growth of the jaw occurs.If this type of treatment fails,the infant then should be considered for other conservative therapies or surgical interventions.This paper reviews surgical interventions such as tongue-lip adhesion,mandibular traction,mandibular distraction,tracheotomy and conservative orthodontic approaches,and presents a baby treated successfully with an orthodontic appliance.
