Diffuse pulmonary lymphangiomatosis （DPL） is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes...Diffuse pulmonary lymphangiomatosis （DPL） is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of the lung. Both the clinical diagnosis and treatment of DPL remain a challenge. Here, we report a case of DPL in a 53-year-old Chinese woman with comprehensive investigations including pulmonary function tests, computer tomography （CT）, bronchoscopy and histological examination of the lung biopsy, and review the literature.展开更多
Lung biopsies examined with light microscope and electron microscope were performed in 34 cases of diffuse pulmonary disease.Open lung biopsy was done in 2 cases,
文摘Diffuse pulmonary lymphangiomatosis （DPL） is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of the lung. Both the clinical diagnosis and treatment of DPL remain a challenge. Here, we report a case of DPL in a 53-year-old Chinese woman with comprehensive investigations including pulmonary function tests, computer tomography （CT）, bronchoscopy and histological examination of the lung biopsy, and review the literature.
文摘Lung biopsies examined with light microscope and electron microscope were performed in 34 cases of diffuse pulmonary disease.Open lung biopsy was done in 2 cases,
