Aim: To report a case of acyanotic Taussig-Bing heart, anatomically consistent with L-transposition and rheumatic Left AV valve regurgitation associated with complete AV block in an adolescent male. Introduction: Taus...Aim: To report a case of acyanotic Taussig-Bing heart, anatomically consistent with L-transposition and rheumatic Left AV valve regurgitation associated with complete AV block in an adolescent male. Introduction: Taussig-Bing heart is one of the conotruncal malformation, characterized by double-outlet right ventricle (DORV) and a subpulmonary VSD. Embryologically, abnormal cardiac looping with malalignment of conotruncal septum result its complexity and great artery relationships. Case Report: A 14-year old acyanotic boy presented with severe left-sided AV valve regurgitation and bradycardia. ECG revealed left sided morphologic right ventricular hypertrophy (RVH) as evidenced by a loss of septal Q waves in left precordial leads suggesting ventricular inversion. X-ray chest revealed a straight upper right cardiac border due to loss of normal relationship of great vessels and cardiomegaly due to both left atrial and morphologic right ventricular enlargements suggesting a left-sided regurgitant lesion. Echocardiography revealed the ventricular inversion, primary origin of both L-transposed great arteries from the left-sided morphologic right ventricle suggesting a “double-outlet morphologic right ventricle” with “double discordance” and a subpulmonary VSD of Taussig-Bing type. The left-sided morphologic tricuspid valve is severely regurgitant due to rheumatic process resulting in heart failure which was improved with anti-failure measures and penicillin prophylaxis. Conclusion: The presence of left-sided regurgitation associated with bradycardia is a suspicion of “double discordance” and “double switch” procedure remains the mainstay of its surgical correction. Left AV valve replacement with intraventricular repair is preferred in this child since the malformation is consistent with Taussing-Bing type of DORV with L-transposition.展开更多
A 23-year-old, lean, scoliotic female presented to our hospital with a history of shortness of breath and cyanosis on exertion. Her 2D echocardiography revealed single left ventricle with both atrio-ventricular valves...A 23-year-old, lean, scoliotic female presented to our hospital with a history of shortness of breath and cyanosis on exertion. Her 2D echocardiography revealed single left ventricle with both atrio-ventricular valves opening in it. She had normally related great arteries, with severe pulmonary artery hypertension, without pulmonary stenosis. Her blood tests indicated that she was reactive to human immunodeficiency virus (HIV-1). The patients died within 2 months despite treatments with anti-retroviral therapy and decongestive therapy.展开更多
The internal flow field of an axial-flow pump under low flow rate conditions is extremely turbulent. The unstable flow region is formed due to the tip leakage and the rotating stall, and is distinguished by a saddle p...The internal flow field of an axial-flow pump under low flow rate conditions is extremely turbulent. The unstable flow region is formed due to the tip leakage and the rotating stall, and is distinguished by a saddle patterned zone in its flow-head curve that demonstrates restrictions in its workable flow range. It is therefore important to understand and improve the operational characteristics of an axial-flow pump under low flow rate conditions. In this study, experiments are performed for the performances of an axial-flow pump at the flow rate in a range between 0.8Qd and 1.2Qd, with the internal flow field measured by the particle image velocimetry (PIV), and with the pump performances and the internal flow field simulated by the Ansys CFX. The simulation results agree well with the experimental results. From the predicted heads at the flow rate in the range between 0.1Qd and 0.7Qd by the numerical simulation, the complete flow-head curves are obtained. The streamlines and the velocity contours in the region in front of the impeller leading edge under different flow conditions are analyzed. By adopting the double-inlet structures, the flow-head characteristics are studied by varying the values of δ and σ respectively, where δ denotes the gap between the inner cylinder end and the impeller leading edge, and σ denotes the gap between the inner cylinder and the outer cylinder. The findings indicate that with the double-inlet design, the velocity distribution can be effectively improved in the region in front of the impeller leading edge, as well as the head performance under the low flow rate conditions, and the positive slope value of the head curve is reduced in the unstable flow range. The optimal δ and σ values are determined.展开更多
ne of premature twins was noticed with thoracoabdominal ectopia cordis and abdominal-walldelect. Purthermore, the mlant was presented with symptoms of tachypnea and moderate cyanosis. Physical examination showed the g...ne of premature twins was noticed with thoracoabdominal ectopia cordis and abdominal-walldelect. Purthermore, the mlant was presented with symptoms of tachypnea and moderate cyanosis. Physical examination showed the giant and pulsating omphalocele measured 40 mm × 50 mm over the anterior abdominal wall. Room air oxygen saturation was 82%. Chest X-ray showed absence of the normal contour of heart in the chest, descensus of the heart to the epigastrium （FigureI A）. Echocardiography visualized abdominal ectopia cordis and double-outlet right ventricle with pulmonary stenosis, the ventricular septal defect and atrial septal defect. Computed tomography （CT） angiography demonstrated a ventral thoracoabdominal wall defect with展开更多
文摘Aim: To report a case of acyanotic Taussig-Bing heart, anatomically consistent with L-transposition and rheumatic Left AV valve regurgitation associated with complete AV block in an adolescent male. Introduction: Taussig-Bing heart is one of the conotruncal malformation, characterized by double-outlet right ventricle (DORV) and a subpulmonary VSD. Embryologically, abnormal cardiac looping with malalignment of conotruncal septum result its complexity and great artery relationships. Case Report: A 14-year old acyanotic boy presented with severe left-sided AV valve regurgitation and bradycardia. ECG revealed left sided morphologic right ventricular hypertrophy (RVH) as evidenced by a loss of septal Q waves in left precordial leads suggesting ventricular inversion. X-ray chest revealed a straight upper right cardiac border due to loss of normal relationship of great vessels and cardiomegaly due to both left atrial and morphologic right ventricular enlargements suggesting a left-sided regurgitant lesion. Echocardiography revealed the ventricular inversion, primary origin of both L-transposed great arteries from the left-sided morphologic right ventricle suggesting a “double-outlet morphologic right ventricle” with “double discordance” and a subpulmonary VSD of Taussig-Bing type. The left-sided morphologic tricuspid valve is severely regurgitant due to rheumatic process resulting in heart failure which was improved with anti-failure measures and penicillin prophylaxis. Conclusion: The presence of left-sided regurgitation associated with bradycardia is a suspicion of “double discordance” and “double switch” procedure remains the mainstay of its surgical correction. Left AV valve replacement with intraventricular repair is preferred in this child since the malformation is consistent with Taussing-Bing type of DORV with L-transposition.
文摘A 23-year-old, lean, scoliotic female presented to our hospital with a history of shortness of breath and cyanosis on exertion. Her 2D echocardiography revealed single left ventricle with both atrio-ventricular valves opening in it. She had normally related great arteries, with severe pulmonary artery hypertension, without pulmonary stenosis. Her blood tests indicated that she was reactive to human immunodeficiency virus (HIV-1). The patients died within 2 months despite treatments with anti-retroviral therapy and decongestive therapy.
基金This work was supported by the Fundamental Research Fund for Central Universities(Grant No.JZ2015HGBZ0129)the Open End Fund of Jiangsu University(Grant No.NRCP201603).
文摘The internal flow field of an axial-flow pump under low flow rate conditions is extremely turbulent. The unstable flow region is formed due to the tip leakage and the rotating stall, and is distinguished by a saddle patterned zone in its flow-head curve that demonstrates restrictions in its workable flow range. It is therefore important to understand and improve the operational characteristics of an axial-flow pump under low flow rate conditions. In this study, experiments are performed for the performances of an axial-flow pump at the flow rate in a range between 0.8Qd and 1.2Qd, with the internal flow field measured by the particle image velocimetry (PIV), and with the pump performances and the internal flow field simulated by the Ansys CFX. The simulation results agree well with the experimental results. From the predicted heads at the flow rate in the range between 0.1Qd and 0.7Qd by the numerical simulation, the complete flow-head curves are obtained. The streamlines and the velocity contours in the region in front of the impeller leading edge under different flow conditions are analyzed. By adopting the double-inlet structures, the flow-head characteristics are studied by varying the values of δ and σ respectively, where δ denotes the gap between the inner cylinder end and the impeller leading edge, and σ denotes the gap between the inner cylinder and the outer cylinder. The findings indicate that with the double-inlet design, the velocity distribution can be effectively improved in the region in front of the impeller leading edge, as well as the head performance under the low flow rate conditions, and the positive slope value of the head curve is reduced in the unstable flow range. The optimal δ and σ values are determined.
文摘ne of premature twins was noticed with thoracoabdominal ectopia cordis and abdominal-walldelect. Purthermore, the mlant was presented with symptoms of tachypnea and moderate cyanosis. Physical examination showed the giant and pulsating omphalocele measured 40 mm × 50 mm over the anterior abdominal wall. Room air oxygen saturation was 82%. Chest X-ray showed absence of the normal contour of heart in the chest, descensus of the heart to the epigastrium （FigureI A）. Echocardiography visualized abdominal ectopia cordis and double-outlet right ventricle with pulmonary stenosis, the ventricular septal defect and atrial septal defect. Computed tomography （CT） angiography demonstrated a ventral thoracoabdominal wall defect with
