Lathosterolosis is a very rare autosomal recessive cholesterol metabolism disorder. The disease manifests itself with developmental and mental delays, learning disabilities, microcephaly, facial dysmorphism, bilateral...Lathosterolosis is a very rare autosomal recessive cholesterol metabolism disorder. The disease manifests itself with developmental and mental delays, learning disabilities, microcephaly, facial dysmorphism, bilateral cataracts, and skeletal defects. It is caused by the deficiency of the enzyme sterol-C5-desaturase, which is involved in cholesterol biosynthesis. This deficiency prevents the synthesis of cholesterol, which acts as a precursor for lipid, bile acids, and steroid hormones. Until 2020, only 7 cases had been reported. In this case report, it was aimed to plan and implement the nursing care of a 2-year-old boy diagnosed with lathosterolosis with the diagnoses of the North American Nursing Diagnostic Association (NANDA).展开更多
Objectives To explore the challenges of secondary use of routinely collected data for analyzing nursing-sensitive outcomes in Austrian acute care hospitals.Method A convergent parallel mixed methods design was perform...Objectives To explore the challenges of secondary use of routinely collected data for analyzing nursing-sensitive outcomes in Austrian acute care hospitals.Method A convergent parallel mixed methods design was performed.We conducted a quantitative representative survey with nursing managers from 32 Austrian general acute care hospitals and 11 qualitative semi-structured interviews with nursing quality management experts.Both results were first analyzed independently and afterward merged in the discussion.Results On average,76%of nursing documentation is already electronically supported in the surveyed Austrian hospitals.However,existing nursing data is seldom used for secondary purposes such as nursing-sensitive outcome analyses.This is due to four major reasons:First,hospitals often do not have a data strategy for the secondary use of routine data.Second,hospitals partly lack the use of standardized and uniform nursing terminologies,especially for nursing evaluation.Third,routine nursing data is often not documented correctly and completely.Fourth,data on nursing-sensitive outcomes is usually collected in specific documentation forms not integrated into routine documentation.Conclusion The awareness of the possibilities for secondary use of nursing data for nursing-sensitive outcome analyses in Austrian hospitals is still in its infancy.Therefore,nursing staff and nursing management must be trained to understand how to collect and process nursing data for nursing-sensitive outcome analyses.Further studies would be interesting in order to determine the factors that influence the decision-making processes for the secondary use of nursing data for outcome analyses.展开更多
文摘Lathosterolosis is a very rare autosomal recessive cholesterol metabolism disorder. The disease manifests itself with developmental and mental delays, learning disabilities, microcephaly, facial dysmorphism, bilateral cataracts, and skeletal defects. It is caused by the deficiency of the enzyme sterol-C5-desaturase, which is involved in cholesterol biosynthesis. This deficiency prevents the synthesis of cholesterol, which acts as a precursor for lipid, bile acids, and steroid hormones. Until 2020, only 7 cases had been reported. In this case report, it was aimed to plan and implement the nursing care of a 2-year-old boy diagnosed with lathosterolosis with the diagnoses of the North American Nursing Diagnostic Association (NANDA).
文摘Objectives To explore the challenges of secondary use of routinely collected data for analyzing nursing-sensitive outcomes in Austrian acute care hospitals.Method A convergent parallel mixed methods design was performed.We conducted a quantitative representative survey with nursing managers from 32 Austrian general acute care hospitals and 11 qualitative semi-structured interviews with nursing quality management experts.Both results were first analyzed independently and afterward merged in the discussion.Results On average,76%of nursing documentation is already electronically supported in the surveyed Austrian hospitals.However,existing nursing data is seldom used for secondary purposes such as nursing-sensitive outcome analyses.This is due to four major reasons:First,hospitals often do not have a data strategy for the secondary use of routine data.Second,hospitals partly lack the use of standardized and uniform nursing terminologies,especially for nursing evaluation.Third,routine nursing data is often not documented correctly and completely.Fourth,data on nursing-sensitive outcomes is usually collected in specific documentation forms not integrated into routine documentation.Conclusion The awareness of the possibilities for secondary use of nursing data for nursing-sensitive outcome analyses in Austrian hospitals is still in its infancy.Therefore,nursing staff and nursing management must be trained to understand how to collect and process nursing data for nursing-sensitive outcome analyses.Further studies would be interesting in order to determine the factors that influence the decision-making processes for the secondary use of nursing data for outcome analyses.
