血栓性血小板减少性紫癜(thrombotic thrombocytopenic purpura,TTP)是一种罕见的、危及生命的血栓性疾病,由血管性血友病因子裂解酶(a disintegrin and metalloproteinase with thrombospondin type 1 motifs 13,ADAMTS13)活性严重缺...血栓性血小板减少性紫癜(thrombotic thrombocytopenic purpura,TTP)是一种罕见的、危及生命的血栓性疾病,由血管性血友病因子裂解酶(a disintegrin and metalloproteinase with thrombospondin type 1 motifs 13,ADAMTS13)活性严重缺乏引起[1]。展开更多
文摘血栓性血小板减少性紫癜(thrombotic thrombocytopenic purpura,TTP)是一种罕见的、危及生命的血栓性疾病,由血管性血友病因子裂解酶(a disintegrin and metalloproteinase with thrombospondin type 1 motifs 13,ADAMTS13)活性严重缺乏引起[1]。