Progressive facial hemiatrophy (PFH) is a ubiquitous disease, characterized by hyperpigmentation of the skin followed by unilateral craniofacial atrophy of su bcutaneous tissues, including fat, muscle and bone. Heredi...Progressive facial hemiatrophy (PFH) is a ubiquitous disease, characterized by hyperpigmentation of the skin followed by unilateral craniofacial atrophy of su bcutaneous tissues, including fat, muscle and bone. Hereditary factors have been postulated to be involved in the aetiology of PFH. Yet, the occurrence of PFH i n one of two identicalmale twins reported heremakes this possibility unlikely. P FH usually occurs in the first two decades of life, and the clinical presentatio n resembles linear scleroderma. PFH may be complicated by autoimmune, neurologic al, ocular and dental disorders. Management of PFH comprises a long term follow -up of somatic disorders, and prevention of psychological problems. Treatment o f PFH is symptomatic and consists of plastic surgery after the disease activity has stopped. Conclusion: The occurrence of PFH in one of a monozygotic twin pair suggests that genetic factors are not involved in its aetiology. Early diagnosi s of PFH and accurate follow-up is essential to disclose the occurrence of comp lications.展开更多
目的:探讨后腹腔镜单侧面游离输尿管切开取石术的临床疗效及应用价值。方法:回顾性分析我院2018年5月—2019年12月65例经后腹腔镜输尿管切开取石术治疗的患者临床资料;将患者分为两组,A组41例接受单侧面纵向游离输尿管切开取石治疗,B组2...目的:探讨后腹腔镜单侧面游离输尿管切开取石术的临床疗效及应用价值。方法:回顾性分析我院2018年5月—2019年12月65例经后腹腔镜输尿管切开取石术治疗的患者临床资料;将患者分为两组,A组41例接受单侧面纵向游离输尿管切开取石治疗,B组24例接受完全游离输尿管切开取石治疗。对两组患者手术时间、术中出血量、术后疼痛反应、伤口引流管留置时间、取石率、住院时间及术后短期并发症情况进行对比分析。结果:两组手术均获得成功,其中A组2例术中结石上移至肾内,改开放手术取石成功;随访6个月两组患者均未出现漏尿、输尿管穿孔等并发症;两组患者在术后疼痛评分[(3.8±1.57)分vs.(4.2±1.25)分,t=1.08,P>0.05]、取石率[95%vs.100%,χ^(2)=0.13,P>0.05]方面差异无统计学意义;与B组比较,A组平均手术时间短[(62.6±12.45) min vs.(73.1±10.62) min,t=3.46,p<0.05]、术中出血量少[(38.9±21.29) mLvs.(54.0±21.47) mL,t=2.74,P<0.05]、伤口引流管留置时间短[(74.9±18.43) h vs.(91.2±19.25) h,t=3.39,P<0.05]、住院时间[(7.3±1.96) d vs.(8.9±1.86) d,t=3.19,P<0.05]。结论:后腹腔镜单侧面纵向游离输尿管切开取石治疗输尿管上段结石效果确切,具有损伤小、手术时间短、康复快等优点,是一种值得临床应用和继续探讨的手术技巧。展开更多
文摘Progressive facial hemiatrophy (PFH) is a ubiquitous disease, characterized by hyperpigmentation of the skin followed by unilateral craniofacial atrophy of su bcutaneous tissues, including fat, muscle and bone. Hereditary factors have been postulated to be involved in the aetiology of PFH. Yet, the occurrence of PFH i n one of two identicalmale twins reported heremakes this possibility unlikely. P FH usually occurs in the first two decades of life, and the clinical presentatio n resembles linear scleroderma. PFH may be complicated by autoimmune, neurologic al, ocular and dental disorders. Management of PFH comprises a long term follow -up of somatic disorders, and prevention of psychological problems. Treatment o f PFH is symptomatic and consists of plastic surgery after the disease activity has stopped. Conclusion: The occurrence of PFH in one of a monozygotic twin pair suggests that genetic factors are not involved in its aetiology. Early diagnosi s of PFH and accurate follow-up is essential to disclose the occurrence of comp lications.
文摘目的:探讨后腹腔镜单侧面游离输尿管切开取石术的临床疗效及应用价值。方法:回顾性分析我院2018年5月—2019年12月65例经后腹腔镜输尿管切开取石术治疗的患者临床资料;将患者分为两组,A组41例接受单侧面纵向游离输尿管切开取石治疗,B组24例接受完全游离输尿管切开取石治疗。对两组患者手术时间、术中出血量、术后疼痛反应、伤口引流管留置时间、取石率、住院时间及术后短期并发症情况进行对比分析。结果:两组手术均获得成功,其中A组2例术中结石上移至肾内,改开放手术取石成功;随访6个月两组患者均未出现漏尿、输尿管穿孔等并发症;两组患者在术后疼痛评分[(3.8±1.57)分vs.(4.2±1.25)分,t=1.08,P>0.05]、取石率[95%vs.100%,χ^(2)=0.13,P>0.05]方面差异无统计学意义;与B组比较,A组平均手术时间短[(62.6±12.45) min vs.(73.1±10.62) min,t=3.46,p<0.05]、术中出血量少[(38.9±21.29) mLvs.(54.0±21.47) mL,t=2.74,P<0.05]、伤口引流管留置时间短[(74.9±18.43) h vs.(91.2±19.25) h,t=3.39,P<0.05]、住院时间[(7.3±1.96) d vs.(8.9±1.86) d,t=3.19,P<0.05]。结论:后腹腔镜单侧面纵向游离输尿管切开取石治疗输尿管上段结石效果确切,具有损伤小、手术时间短、康复快等优点,是一种值得临床应用和继续探讨的手术技巧。
