A 3- year- old boy associated with Opitz syndrome including hypospadia and anorectal anomaly was transferred to Osaka University Hospital with orotracheal intubation because of respiratory distress after respiratory i...A 3- year- old boy associated with Opitz syndrome including hypospadia and anorectal anomaly was transferred to Osaka University Hospital with orotracheal intubation because of respiratory distress after respiratory infection. He had l aryngeal cleft diagnosed in the neonatal period because of symptoms including st ridor and aspiration. After 2 attempts at extubation, tracheostomy was performed . Fiberscopic examination demonstrated obstruction of the airway from the vocal cord to subglottic space by inspired esophageal redundant mucosa. There was no i mprovement observed for 3 months. He underwent anterior repair of cleft, anterio r laryngotracheoplasty with costal cartilage graft, closure of tracheostomy, and endoscopic Nissen fundoplication. The postoperative course during the subsequen t year was uneventful without feeding or speaking disorders. Subglottic airway o bstruction caused by inspired redundant mucosa is a rare complication in larynge al cleft. Anterior laryngotracheoplasty and Nissen fundoplication should be cons idered for this complication, in addition to the usual procedure for cleft repai r.展开更多
文摘A 3- year- old boy associated with Opitz syndrome including hypospadia and anorectal anomaly was transferred to Osaka University Hospital with orotracheal intubation because of respiratory distress after respiratory infection. He had l aryngeal cleft diagnosed in the neonatal period because of symptoms including st ridor and aspiration. After 2 attempts at extubation, tracheostomy was performed . Fiberscopic examination demonstrated obstruction of the airway from the vocal cord to subglottic space by inspired esophageal redundant mucosa. There was no i mprovement observed for 3 months. He underwent anterior repair of cleft, anterio r laryngotracheoplasty with costal cartilage graft, closure of tracheostomy, and endoscopic Nissen fundoplication. The postoperative course during the subsequen t year was uneventful without feeding or speaking disorders. Subglottic airway o bstruction caused by inspired redundant mucosa is a rare complication in larynge al cleft. Anterior laryngotracheoplasty and Nissen fundoplication should be cons idered for this complication, in addition to the usual procedure for cleft repai r.
