ANGIOSARCOMA is the most common primary malignant cardiac tumor. Until recently, the diagnosis is often not established until the tumor is advanced with vital cardiac structure involved or distal metastasis, mainly be...ANGIOSARCOMA is the most common primary malignant cardiac tumor. Until recently, the diagnosis is often not established until the tumor is advanced with vital cardiac structure involved or distal metastasis, mainly because the symptoms are initially nonspecific. The natural history of cardiac angiosarcoma is characterized by a short clinical course and a fatal outcome. Surgical resection remains the preferential therapy for palliation or cure, whereas irradiation and chemotherapy have only limited use. We herein reported a successful radical resection of cardiac angiosarcoma with concomitant reconstruction of right coronary artery, tricuspid leaflet, and atrial wall. The literature on cardiac angiosarcomas is reviewed extensively, with emphasis on presentation and surgical management.展开更多
文摘ANGIOSARCOMA is the most common primary malignant cardiac tumor. Until recently, the diagnosis is often not established until the tumor is advanced with vital cardiac structure involved or distal metastasis, mainly because the symptoms are initially nonspecific. The natural history of cardiac angiosarcoma is characterized by a short clinical course and a fatal outcome. Surgical resection remains the preferential therapy for palliation or cure, whereas irradiation and chemotherapy have only limited use. We herein reported a successful radical resection of cardiac angiosarcoma with concomitant reconstruction of right coronary artery, tricuspid leaflet, and atrial wall. The literature on cardiac angiosarcomas is reviewed extensively, with emphasis on presentation and surgical management.
