泛发性皮肤肥大细胞增生病4例报告

泛发型皮肤肥大细胞增生病又称色素性荨麻疹(Urtricaria pigmeentosa),是肥大细胞增生病中良性类皮肤型的一种,依其发病的迟早及临床表现的不同,分为幼年型(早发型)及成年型(迟发型)。本病较为少见。

皮肤泛发性肥大细胞增生症1例

患儿男,6个月。生后一周左下肢起红色斑,逐渐形成水疱,破后结痂,脱痂后逐渐隆起形成结节。半年来皮损不断增多,发展到胸,背、上肢、手足及头面等处。常哭闹,好动,不自主搔抓皮损。不发烧。食、眠,二便正常。因当地诊断不清,经抗生素、脱敏药治疗不愈来我门诊就医。

一儿科系统性肥大细胞增多症患者出现复发性昏厥伴过敏反应:病例报道及文献综述

Mastocytosis refers to a rare collection of disorders, both cutaneous and systemic, that are characterized by increased numbersof mast cells. Depending on the extent of the disease, these disorders may present with symptoms resulting from mast cell degranulation including flushing, diarrhea, vomiting, cramping,syncope, or anaphylaxis. In pediatric patients, cutaneous involvement is most prevalent in the form of urticaria pigmentosa ,which is typically asymptomatic or minimally so with resolution by adolescence. In this case report and review of literature, we review a case of a 3-year-old child with uritcaria pigmentosa displaying recurrent syncope and anaphylaxis as the first presentation of systemic mastocytosis. We found data to be limited on this topic, and concluded that pediatric patients with prior diagnoses of cutaneous mastocytosis could benefit from either more aggressive screening for systemic disease or prophylactic treatment with antihistamines and rescue subcutaneous epinephrine.

泛发性家族性慢性良性天疱疮一家系

临床资料先证者男，67岁。因皮肤皱褶处反复发生浸渍、糜烂近40年就诊。患者40年前双侧腹股沟及腋窝无明显诱因出现红斑、水疱，水疱破溃后形成浅表糜烂、结痂。随后皮疹范围扩大，逐渐累及腋窝、胭窝、颈部、前胸及脐周。反复发生皮疹后，在皮疹处形成浅表疣状增生，表面粗糙伴潮湿。

56例重症银屑病患者的护理体会

银屑病是一种常见的以表皮增生为特征的慢性复发性炎症性皮肤病。临床上通常将泛发性脓疱型银屑病、关节病型银屑病和红皮病型银屑病称为重症银屑病。重症银屑病的症状主要表现为全身肿痛、发热、部分皮肤潮红、皮损遍布全身等。我院自2008年3月至2011年12月共收治重症银屑病患者56例，经护理人员精心护理，均痊愈出院，现将护理体会总结如下。

持久性发疹性斑状毛细血管扩张症一例

持久性发疹性斑状毛细血管扩张症（telangiectasia macularis eruptiva perstans,TMEP）属于皮肤型肥大细胞增生症（cutaneous mastocytosis CM）中的一种类型,相对罕见,临床表现多样。现报道本院诊治的一例患者。临床资料患者,女,43岁,造纸工人。躯干多发性褐色斑丘疹14年,逐渐增多并累及面颈部、四肢5年余。