Background: Bladder exstrophy is a rare congenital malformation of the genitourinary system, with an estimated incidence of approximately 1 per 50,000 live births. Clinically, patients do not have capacity to accumula...Background: Bladder exstrophy is a rare congenital malformation of the genitourinary system, with an estimated incidence of approximately 1 per 50,000 live births. Clinically, patients do not have capacity to accumulate urine and urine continously leak. We present patient with partial storing capacity from the dialated distal ureters. A case of dialated distal ureters from an 8-year-old female patient with ectopic vesicae is described. The dialated ureters act as reservoir of urine where the patient is partially continent in the night time. These dialated ureters are the compensation for the literally absent bladder. During reconstruction, we observed that they can be used as an additional bladder volume reducing risk of reconstruction failure from tension.展开更多
[目的]探讨经尿道等离子膀胱肿瘤电切术(TURBT) 联合吡柔比星灌注治疗浅表性膀胱癌的安全性与有效性.[方法]用经尿道等离子体双极电切系统膀胱肿瘤电切(transurethral resection of the bladder tumor,TURBT)治疗膀胱癌90例,肿瘤分...[目的]探讨经尿道等离子膀胱肿瘤电切术(TURBT) 联合吡柔比星灌注治疗浅表性膀胱癌的安全性与有效性.[方法]用经尿道等离子体双极电切系统膀胱肿瘤电切(transurethral resection of the bladder tumor,TURBT)治疗膀胱癌90例,肿瘤分级G1为72例,G2为18例.电极切除肿瘤直达深肌层,同时扩大到电切距肿瘤基底1 cm范围的正常组织,术后定期进行膀胱内灌注吡柔比星化疗.[结果]手术时间5~46 min,平均(14±12) min.术中无经尿道电切综合征,发生闭孔神经反射11例,其中腹膜外穿孔1例.随访3~24 个月,8例复发,7例再行TURBT,1例并发尿道移形上皮癌,并行全尿道切除术,术后追踪观察至今未复发.[结论]TURBT联合吡柔比星膀胱灌注是治疗浅表性膀胱癌是的一种理想方法,疗效好,创伤小,副反应低,值得推广应用.展开更多
文摘Background: Bladder exstrophy is a rare congenital malformation of the genitourinary system, with an estimated incidence of approximately 1 per 50,000 live births. Clinically, patients do not have capacity to accumulate urine and urine continously leak. We present patient with partial storing capacity from the dialated distal ureters. A case of dialated distal ureters from an 8-year-old female patient with ectopic vesicae is described. The dialated ureters act as reservoir of urine where the patient is partially continent in the night time. These dialated ureters are the compensation for the literally absent bladder. During reconstruction, we observed that they can be used as an additional bladder volume reducing risk of reconstruction failure from tension.