Bland-White-Garland syndrome is a rare syndrome with anomalous origin of the left coronary artery (LCA) arising from the pulmonary artery, resulting in left ventricular failure. It could occur shortly after birth. We ...Bland-White-Garland syndrome is a rare syndrome with anomalous origin of the left coronary artery (LCA) arising from the pulmonary artery, resulting in left ventricular failure. It could occur shortly after birth. We here reported the case of a 6-week-old boy with aortostenosis. Coronary angiography revealed an anomalous LCA arising from the pulmonary artery. Representation of a prominent right coronary artery (RCA) delivered numerous collateral vessels to the LCA area.The patient underwent a correction operation with translocation of the LCA and re-implantation into the ascending aorta. One month after operation, clear decrease in the expanded ventricle was noted with an increase in the contractibility.展开更多
Objective: To make a pictorial presentation of the anomalous origin of left coronary artery arising from the pulmonary artery (ALCAPA) appearances in adults on MDCT angiography. Methods: A retrospective evaluation was...Objective: To make a pictorial presentation of the anomalous origin of left coronary artery arising from the pulmonary artery (ALCAPA) appearances in adults on MDCT angiography. Methods: A retrospective evaluation was performed between 2005 and 2011 by ECG-gated coronary MDCT angiography. Total 8 patients included (9-51 years, mean age 29 years, 7 female). Image quality was evaluated firstly. Multi planar reformations (MPRs), maximum intensity projections (MIPs) and 3D volume-rendering techniques were used to evaluate image features. In addition, right and left coronary artery orifices were measured for each case. Results: Total 8/70,000 cases diagnosed ALCAPA by MDCT exam, all image qualities were acceptable. As the diagnose key point, all left coronary artery origin were clearly described, and indirect signs such as dilated and tortuous right/left arteries and collateral vessels between them, enlarged left ventricle were also well showed, the dilated degree of both the RCA and the LCA were marked with ages, the diameter of RCA for each case were a mild wider than that of left one. Other combined signs like papillary muscle calcification, bronchial arteries from aorta to the cardiac and coronary artery degeneration change were also included by MDCT angiography findings in a single data acquisition. No combined inter cardiac malformations in our group. Conclusion: ECG-gated MDCT an-giography plays an important role as a first-line modality in assessment of ALCAPA.展开更多
1病例资料患者,女,49岁,主因"间断胸闷、心悸、乏力40余年,加重10 d"于2019年6月20日就诊于我院。患者于40余年前间断出现胸闷、心悸、乏力症状,未系统诊治,15余年前于辽宁省人民医院诊断为左冠状动脉异常起源于肺动脉(anomal...1病例资料患者,女,49岁,主因"间断胸闷、心悸、乏力40余年,加重10 d"于2019年6月20日就诊于我院。患者于40余年前间断出现胸闷、心悸、乏力症状,未系统诊治,15余年前于辽宁省人民医院诊断为左冠状动脉异常起源于肺动脉(anomalous left coronary artery from the pulmonary artery,ALCAPA),行左冠状动脉异位起源纠正术,术中探查见右冠状动脉显著扩张、迂曲,左冠状动脉及左主干扩张,遂结扎异常起源的左冠状动脉并行以大隐静脉为移植物的冠状动脉旁路移植术,术后规律随访4余年,无明显临床症状。展开更多
文摘Bland-White-Garland syndrome is a rare syndrome with anomalous origin of the left coronary artery (LCA) arising from the pulmonary artery, resulting in left ventricular failure. It could occur shortly after birth. We here reported the case of a 6-week-old boy with aortostenosis. Coronary angiography revealed an anomalous LCA arising from the pulmonary artery. Representation of a prominent right coronary artery (RCA) delivered numerous collateral vessels to the LCA area.The patient underwent a correction operation with translocation of the LCA and re-implantation into the ascending aorta. One month after operation, clear decrease in the expanded ventricle was noted with an increase in the contractibility.
文摘Objective: To make a pictorial presentation of the anomalous origin of left coronary artery arising from the pulmonary artery (ALCAPA) appearances in adults on MDCT angiography. Methods: A retrospective evaluation was performed between 2005 and 2011 by ECG-gated coronary MDCT angiography. Total 8 patients included (9-51 years, mean age 29 years, 7 female). Image quality was evaluated firstly. Multi planar reformations (MPRs), maximum intensity projections (MIPs) and 3D volume-rendering techniques were used to evaluate image features. In addition, right and left coronary artery orifices were measured for each case. Results: Total 8/70,000 cases diagnosed ALCAPA by MDCT exam, all image qualities were acceptable. As the diagnose key point, all left coronary artery origin were clearly described, and indirect signs such as dilated and tortuous right/left arteries and collateral vessels between them, enlarged left ventricle were also well showed, the dilated degree of both the RCA and the LCA were marked with ages, the diameter of RCA for each case were a mild wider than that of left one. Other combined signs like papillary muscle calcification, bronchial arteries from aorta to the cardiac and coronary artery degeneration change were also included by MDCT angiography findings in a single data acquisition. No combined inter cardiac malformations in our group. Conclusion: ECG-gated MDCT an-giography plays an important role as a first-line modality in assessment of ALCAPA.
文摘1病例资料患者,女,49岁,主因"间断胸闷、心悸、乏力40余年,加重10 d"于2019年6月20日就诊于我院。患者于40余年前间断出现胸闷、心悸、乏力症状,未系统诊治,15余年前于辽宁省人民医院诊断为左冠状动脉异常起源于肺动脉(anomalous left coronary artery from the pulmonary artery,ALCAPA),行左冠状动脉异位起源纠正术,术中探查见右冠状动脉显著扩张、迂曲,左冠状动脉及左主干扩张,遂结扎异常起源的左冠状动脉并行以大隐静脉为移植物的冠状动脉旁路移植术,术后规律随访4余年,无明显临床症状。
