BACKGROUND Cor triatriatum sinistrum or cor triatriatum sinister is a rare congenital heart disease that accounts for approximately 0.1%of all cardiac abnormalities.It is defined as the presence of an anomalous septum...BACKGROUND Cor triatriatum sinistrum or cor triatriatum sinister is a rare congenital heart disease that accounts for approximately 0.1%of all cardiac abnormalities.It is defined as the presence of an anomalous septum that divides the left atrium into two cavities,and in most cases,it can be asymptomatic or less frequently very severe.CASE SUMMARY A 37-year-old pregnant woman visited our hospital.In the first trimester scan,we detected signs of fluid in the pericardium(pericardial effusion)that reached the atriums.In the third trimester,an anomalous septum in the left atrium suspicious of cor triatriatum sinister was detected.Expectant management was decided,the pregnancy evolved normally and resulted in uncomplicated delivery of a healthy child.The findings in the prenatal scan were confirmed by echocardiography and the diagnosis of cor triatriatum sinister was confirmed.The newborn was asymptomatic at all times.CONCLUSION We show expectant management of cor triatriatum sinister and suggest an association between this entity and early pericardial effusion.展开更多
Cor-triatriatum dexter is an extremely rare congenital anomaly, in which right atrium is divided into 2 halves by a septum giving rise to 3 atrial chambers. We report here a case of cor-triatriatum dexter who presente...Cor-triatriatum dexter is an extremely rare congenital anomaly, in which right atrium is divided into 2 halves by a septum giving rise to 3 atrial chambers. We report here a case of cor-triatriatum dexter who presented at 3 days of life with tachypnea and did not respond to antibiotics. Echocardiography revealed ostium secundum atrial septal defect (ASD) with right to left flow, intact interventricular septum (IVS), severe tricuspid regurgitation with pulmonary arterial hypertension and a membranous structure dividing right atrium into 2 halves with good biventricular function. The patient improved with sildenafil and anti-failure medication. This case of cor-triatriatum dexter presenting with pulmonary hypertension, tricuspid regurgitation and ASD added to the new spectrum of cor-triatriatum dexter.展开更多
文摘BACKGROUND Cor triatriatum sinistrum or cor triatriatum sinister is a rare congenital heart disease that accounts for approximately 0.1%of all cardiac abnormalities.It is defined as the presence of an anomalous septum that divides the left atrium into two cavities,and in most cases,it can be asymptomatic or less frequently very severe.CASE SUMMARY A 37-year-old pregnant woman visited our hospital.In the first trimester scan,we detected signs of fluid in the pericardium(pericardial effusion)that reached the atriums.In the third trimester,an anomalous septum in the left atrium suspicious of cor triatriatum sinister was detected.Expectant management was decided,the pregnancy evolved normally and resulted in uncomplicated delivery of a healthy child.The findings in the prenatal scan were confirmed by echocardiography and the diagnosis of cor triatriatum sinister was confirmed.The newborn was asymptomatic at all times.CONCLUSION We show expectant management of cor triatriatum sinister and suggest an association between this entity and early pericardial effusion.
文摘Cor-triatriatum dexter is an extremely rare congenital anomaly, in which right atrium is divided into 2 halves by a septum giving rise to 3 atrial chambers. We report here a case of cor-triatriatum dexter who presented at 3 days of life with tachypnea and did not respond to antibiotics. Echocardiography revealed ostium secundum atrial septal defect (ASD) with right to left flow, intact interventricular septum (IVS), severe tricuspid regurgitation with pulmonary arterial hypertension and a membranous structure dividing right atrium into 2 halves with good biventricular function. The patient improved with sildenafil and anti-failure medication. This case of cor-triatriatum dexter presenting with pulmonary hypertension, tricuspid regurgitation and ASD added to the new spectrum of cor-triatriatum dexter.
