Hereditary haemorrhagic telangiectasia(HHT)is an autosomal,predominantly inherited disease characterized by diffuse telangiectases involving the skin,mucous membranes,lung,brain,gastrointestinal tract and liver.Pelios...Hereditary haemorrhagic telangiectasia(HHT)is an autosomal,predominantly inherited disease characterized by diffuse telangiectases involving the skin,mucous membranes,lung,brain,gastrointestinal tract and liver.Peliosis hepatis is a rare,benign disorder causing sinusoidal dilatation and the presence of multiple blood-filled lacunar spaces within the liver.We report a case of an HHT patient with incidental magnetic resonance findings of focal hepatic peliosis.展开更多
文摘Hereditary haemorrhagic telangiectasia(HHT)is an autosomal,predominantly inherited disease characterized by diffuse telangiectases involving the skin,mucous membranes,lung,brain,gastrointestinal tract and liver.Peliosis hepatis is a rare,benign disorder causing sinusoidal dilatation and the presence of multiple blood-filled lacunar spaces within the liver.We report a case of an HHT patient with incidental magnetic resonance findings of focal hepatic peliosis.