Background: Vanishing lung is a rare syndrome. It mainly affects young males who are smokers, it considered an advanced stage of bullous disease, where the entire lobe or lung paranchym is replaced by bullae, it appea...Background: Vanishing lung is a rare syndrome. It mainly affects young males who are smokers, it considered an advanced stage of bullous disease, where the entire lobe or lung paranchym is replaced by bullae, it appears radiologically as a hyperlucency due to air trapping and destruction of interstitial tissue and vascularity in alveolar wall’s. Misdiagnosed usually as pneumothorax so must be differentiated from other causes of Hyperlucency lung syndrom. Hereby a case of vanishing lung diagnosed primarily as a post TB lung destruction. Case Report: A sixteenth-year-old virgin female patient, with treated for TB for six months without radilogical improvement. CXR and CT scan revealed diffuse left lung hyperlucency, TB work up (sputum exam, washing by bronchoscopy) appears no active disease. Left pneumenctomy had done, grossly there are no lung pranchyma and microscopically no signs of TB in the specimen. The findings are consistent with Vanishing lung. Conclusions: An understanding of the broad differential diagnosis of pulmonary hyperlucency is necessary to determine the underlying cause and provide appropriate patient care.展开更多
Swyer-James-MacLeod syndrome is a rare disease that results in parenchymal damage believed to be caused by recurrent lung infections in childhood. We report a case of a previously healthy young woman that presented wi...Swyer-James-MacLeod syndrome is a rare disease that results in parenchymal damage believed to be caused by recurrent lung infections in childhood. We report a case of a previously healthy young woman that presented with insidious progression of exertional dyspnea with restrictive lung physiology. Axial imaging demonstrated a hyperinflated emphysematous right lung with lower lobe fibrosis, nodules and air-fluid filled cysts, with a small right pulmonary artery and contralateral shifting of the mediastinum. She underwent right pneumonectomy ultimately resulting in improvement of her symptoms, with surgical pathology indicating extensive emphysema, bronchiec- tasis, fibrosis with osseous metaplasia, and placental transmogrification of alveolar septa, being consistent with a diagnosis of SJMS.展开更多
文摘Background: Vanishing lung is a rare syndrome. It mainly affects young males who are smokers, it considered an advanced stage of bullous disease, where the entire lobe or lung paranchym is replaced by bullae, it appears radiologically as a hyperlucency due to air trapping and destruction of interstitial tissue and vascularity in alveolar wall’s. Misdiagnosed usually as pneumothorax so must be differentiated from other causes of Hyperlucency lung syndrom. Hereby a case of vanishing lung diagnosed primarily as a post TB lung destruction. Case Report: A sixteenth-year-old virgin female patient, with treated for TB for six months without radilogical improvement. CXR and CT scan revealed diffuse left lung hyperlucency, TB work up (sputum exam, washing by bronchoscopy) appears no active disease. Left pneumenctomy had done, grossly there are no lung pranchyma and microscopically no signs of TB in the specimen. The findings are consistent with Vanishing lung. Conclusions: An understanding of the broad differential diagnosis of pulmonary hyperlucency is necessary to determine the underlying cause and provide appropriate patient care.
文摘Swyer-James-MacLeod syndrome is a rare disease that results in parenchymal damage believed to be caused by recurrent lung infections in childhood. We report a case of a previously healthy young woman that presented with insidious progression of exertional dyspnea with restrictive lung physiology. Axial imaging demonstrated a hyperinflated emphysematous right lung with lower lobe fibrosis, nodules and air-fluid filled cysts, with a small right pulmonary artery and contralateral shifting of the mediastinum. She underwent right pneumonectomy ultimately resulting in improvement of her symptoms, with surgical pathology indicating extensive emphysema, bronchiec- tasis, fibrosis with osseous metaplasia, and placental transmogrification of alveolar septa, being consistent with a diagnosis of SJMS.
