这盏被称为light au lait的壁灯由Ingo Maurer和FabienDumas设计完成。这是一盏具有异想天开色彩的壁灯,它模糊了家具的功能性和艺术性。杯子成了壁灯的灯罩,碟子成了固定在墙上的依托和装饰,而勺子则成了具有艺术色彩的拉线。设计师通...这盏被称为light au lait的壁灯由Ingo Maurer和FabienDumas设计完成。这是一盏具有异想天开色彩的壁灯,它模糊了家具的功能性和艺术性。杯子成了壁灯的灯罩,碟子成了固定在墙上的依托和装饰,而勺子则成了具有艺术色彩的拉线。设计师通过令人意想不到的方式展现了咖啡杯的形象,同时也有了这个非常有趣的设计。展开更多
Neurofibromatosis Type 1 (NF-1 or Von Recklinghausen disease) is an autosomal dominant genetic disease, characterized by an extreme variability of its clinical expression which is also found in the same family. Our wo...Neurofibromatosis Type 1 (NF-1 or Von Recklinghausen disease) is an autosomal dominant genetic disease, characterized by an extreme variability of its clinical expression which is also found in the same family. Our work focuses on the exploitation of four cases of patients with NF-1 who were enrolled in the paediatric neurology consultation at Rabat Children’s Hospital. They are two infants and two children. Otherwise the diagnosis was made in front of the existence of café au lait and lentiginous spots in two boys, also the existence of café au lait spots and abnormalities in brain imaging in two girls. Thus an evolution was marked by a favorable outcome for three patients and neurological sequelae in one patient.展开更多
文摘这盏被称为light au lait的壁灯由Ingo Maurer和FabienDumas设计完成。这是一盏具有异想天开色彩的壁灯,它模糊了家具的功能性和艺术性。杯子成了壁灯的灯罩,碟子成了固定在墙上的依托和装饰,而勺子则成了具有艺术色彩的拉线。设计师通过令人意想不到的方式展现了咖啡杯的形象,同时也有了这个非常有趣的设计。
文摘Neurofibromatosis Type 1 (NF-1 or Von Recklinghausen disease) is an autosomal dominant genetic disease, characterized by an extreme variability of its clinical expression which is also found in the same family. Our work focuses on the exploitation of four cases of patients with NF-1 who were enrolled in the paediatric neurology consultation at Rabat Children’s Hospital. They are two infants and two children. Otherwise the diagnosis was made in front of the existence of café au lait and lentiginous spots in two boys, also the existence of café au lait spots and abnormalities in brain imaging in two girls. Thus an evolution was marked by a favorable outcome for three patients and neurological sequelae in one patient.
