Background: Congenital Mesoblastic Nephroma (CMN) is a mesenchymal renal tumour of early life. With a median diagnosis of two months and over 90% of cases occurring within the first year of life, it is the most preval...Background: Congenital Mesoblastic Nephroma (CMN) is a mesenchymal renal tumour of early life. With a median diagnosis of two months and over 90% of cases occurring within the first year of life, it is the most prevalent non-Wilms’ renal tumour. Even though imaging can be used as a diagnosing tool, it is frequently identified in the neonatal period when the baby has an abdominal mass. There are three different histologic types: mixed, cellular, and classic. Radical nephrectomy is the usual mode of treatment, though adjuvant chemotherapy may be necessary for the cellular type, which may be aggressive. Case presentation: We report on a case of a 2-day-old term male neonate born to a 27-year-old mother through spontaneous vertex delivery (SVD). He presented with a right-sided abdominal mass from birth. An abdominal ultrasound scan revealed a huge, well-circumscribed heterogeneous soft tissue mass in the right hemi-abdomen extending to the left side, measuring 10.2 cm by 8.0 cm. He underwent a right radical nephrectomy with a tumour weight of 450 g and a size of 18 cm × 15 cm × 6 cm. Histopathological diagnosis was Congenital Mesoblastic Nephroma (cellular type) Stage 1. Conclusion: Any infant with a renal tumour should be evaluated for congenital mesoblastic nephroma. Detailed investigation and complete resection are fundamental for ensuring an excellent outcome.展开更多
Cystic nephromas (CNs) are uncommon, benign renal neoplasms reported in infants/young children of both genders and in adult females, concerning the pediatric population few studies have been conducted. The diagnosis o...Cystic nephromas (CNs) are uncommon, benign renal neoplasms reported in infants/young children of both genders and in adult females, concerning the pediatric population few studies have been conducted. The diagnosis of cystic nephroma is based on clinical signs, imaging tests, and anatomo-pathological study. In children, CNs can appear as a palpable abdominal mass in most of cases, hematuria or recurrent urinary infections. They are characterized by multycystic architecture and the exclusive presence of mature nephrogenic elements. Treatment is surgical with a very good prognosis in most of cases. We are going to report a case of a 13-month-old girl child diagnosed with Cystic nephromas who presented to pediatric emergency with unexplained crying episodes in order to increase clinicians awareness about this rare tumor.展开更多
Cystic nephroma is a rare benign renal lesion with non-specific presenting symptoms.This tumour has a bimodal age distribution presenting in children between 3 months and 2 years and in adults over 30 years of age.The...Cystic nephroma is a rare benign renal lesion with non-specific presenting symptoms.This tumour has a bimodal age distribution presenting in children between 3 months and 2 years and in adults over 30 years of age.There is male preponderance with a 2:1 male to female ratio in the childhood whereas it is commoner in females in adults.It is uncommon in the age-group of 5 yearse30 years.We describe a case of cystic nephroma in a 25-year-old female which was managed by partial nephrectomy.展开更多
文摘Background: Congenital Mesoblastic Nephroma (CMN) is a mesenchymal renal tumour of early life. With a median diagnosis of two months and over 90% of cases occurring within the first year of life, it is the most prevalent non-Wilms’ renal tumour. Even though imaging can be used as a diagnosing tool, it is frequently identified in the neonatal period when the baby has an abdominal mass. There are three different histologic types: mixed, cellular, and classic. Radical nephrectomy is the usual mode of treatment, though adjuvant chemotherapy may be necessary for the cellular type, which may be aggressive. Case presentation: We report on a case of a 2-day-old term male neonate born to a 27-year-old mother through spontaneous vertex delivery (SVD). He presented with a right-sided abdominal mass from birth. An abdominal ultrasound scan revealed a huge, well-circumscribed heterogeneous soft tissue mass in the right hemi-abdomen extending to the left side, measuring 10.2 cm by 8.0 cm. He underwent a right radical nephrectomy with a tumour weight of 450 g and a size of 18 cm × 15 cm × 6 cm. Histopathological diagnosis was Congenital Mesoblastic Nephroma (cellular type) Stage 1. Conclusion: Any infant with a renal tumour should be evaluated for congenital mesoblastic nephroma. Detailed investigation and complete resection are fundamental for ensuring an excellent outcome.
文摘Cystic nephromas (CNs) are uncommon, benign renal neoplasms reported in infants/young children of both genders and in adult females, concerning the pediatric population few studies have been conducted. The diagnosis of cystic nephroma is based on clinical signs, imaging tests, and anatomo-pathological study. In children, CNs can appear as a palpable abdominal mass in most of cases, hematuria or recurrent urinary infections. They are characterized by multycystic architecture and the exclusive presence of mature nephrogenic elements. Treatment is surgical with a very good prognosis in most of cases. We are going to report a case of a 13-month-old girl child diagnosed with Cystic nephromas who presented to pediatric emergency with unexplained crying episodes in order to increase clinicians awareness about this rare tumor.
文摘Cystic nephroma is a rare benign renal lesion with non-specific presenting symptoms.This tumour has a bimodal age distribution presenting in children between 3 months and 2 years and in adults over 30 years of age.There is male preponderance with a 2:1 male to female ratio in the childhood whereas it is commoner in females in adults.It is uncommon in the age-group of 5 yearse30 years.We describe a case of cystic nephroma in a 25-year-old female which was managed by partial nephrectomy.
