BACKGROUND Congenital biliary atresia is a type of obstruction of the bile ducts inside and outside the liver,which can lead to cholestatic liver cirrhosis and eventually liver failure.The preduodenal portal vein(PD-P...BACKGROUND Congenital biliary atresia is a type of obstruction of the bile ducts inside and outside the liver,which can lead to cholestatic liver cirrhosis and eventually liver failure.The preduodenal portal vein(PD-PV)is a rare developmental malformation of the PV.The PV courses in front of the duodenum.However,very few cases of neonatal biliary atresia combined with PD-PV have been reported in the scientific literature.CASE SUMMARY A 1-mo-and-4-d-old child was admitted to the hospital in January because of yellowish skin.After surgical consultation,surgical intervention was recommended.The child underwent Hilar-jejunal anastomosis,duodenal rhomboid anastomosis,and abdominal drainage under general anesthesia.During the operation,the PV was located at the anterior edge of the duodenum.CONCLUSION Diagnoses:(1)Congenital biliary atresia;(2)PD-PV;and(3)Congenital cardiovascular malformations.Outcomes:Recommendation for liver transplantation.Lessons:The choice of treatment options for neonatal biliary atresia combined with PD-PV.展开更多
基金The Science Foundation of Suzhou Science and Technology Bureau,No.SYS201758 and No.SYS2020158and Youth Science and technology project of revitalizing health by science and education in Suzhou in 2019,No.KJXW2019020.
文摘BACKGROUND Congenital biliary atresia is a type of obstruction of the bile ducts inside and outside the liver,which can lead to cholestatic liver cirrhosis and eventually liver failure.The preduodenal portal vein(PD-PV)is a rare developmental malformation of the PV.The PV courses in front of the duodenum.However,very few cases of neonatal biliary atresia combined with PD-PV have been reported in the scientific literature.CASE SUMMARY A 1-mo-and-4-d-old child was admitted to the hospital in January because of yellowish skin.After surgical consultation,surgical intervention was recommended.The child underwent Hilar-jejunal anastomosis,duodenal rhomboid anastomosis,and abdominal drainage under general anesthesia.During the operation,the PV was located at the anterior edge of the duodenum.CONCLUSION Diagnoses:(1)Congenital biliary atresia;(2)PD-PV;and(3)Congenital cardiovascular malformations.Outcomes:Recommendation for liver transplantation.Lessons:The choice of treatment options for neonatal biliary atresia combined with PD-PV.
