OBJECTIVE: To describe a case of Ehlers-Danlos syndrome type IV and its pedigree in China. METHODS: Clinical materials of a case of Ehlers-Danlos syndrome type IV and a pedigree of 6 members within 4 generations were ...OBJECTIVE: To describe a case of Ehlers-Danlos syndrome type IV and its pedigree in China. METHODS: Clinical materials of a case of Ehlers-Danlos syndrome type IV and a pedigree of 6 members within 4 generations were analyzed. Dilated internal jugular vein in the proband was removed by operation. The diagnosis, surgical treatment, and postoperative complications were retrospectively reviewed. RESULTS: Vessels of the proband in the pedigree were crisp and easily lacinated during the procedure of removing his internal jugular vein. Repeating postoperative hematomas were found though complete stanching was achieved during the operation. The patient was successfully recovered by promptly debridgement and needle sucking. The other 5 members of the pedigree all had the triads of Ehlers-Danlos syndrome. CONCLUSIONS: Though it was of extremely low morbidity rate, the high mortality rate and complication of Ehlers-Danlos syndrome deserve great attention during surgical management, especially in patients with Ehlers-Danlos syndrome type IV. Surgeons should be aware of the ponderance of its complications and combined diseases to avoid fatal intraoperative vascular lascination and incontrollable hemorrhage.展开更多
Chinese Traditional Maps and Local Chronicles serve as significant sources for investigating the urban history of ancient Chinese cities.These documents prioritize the abstract representation of topological relationsh...Chinese Traditional Maps and Local Chronicles serve as significant sources for investigating the urban history of ancient Chinese cities.These documents prioritize the abstract representation of topological relationships over precise numerical values and geometric shapes.This is consistent with the traditional Chinese city image and spatial schema emphasizing“harmony between man and nature”.Most Chinese Traditional Maps reflect a centripetal spatial schema,wherein the core area is located at the center,and other locations are positioned hierarchically about the center.Based on this data,this research aims to categorize and examine the development and evolution of the centripetal spatial schema in ancient Chinese cities by constructing a pedigree of types.The authors identify three types and summarize their causes,calculate the topological features,and reveal their correlations with the type of pedigree.This study reveals that cities with different centripetal forms exhibit regular differences in the accessibility,centrality,and functional attributes of central nodes,as well as the proportion of nodes with different attributes in the city.Overall,the conclusion aims to deepen people’s understanding of traditional Chinese spatial concepts at the macro-urban level,particularly in the context of China’s current urban renewal wave.Additionally,it provides practical references for inheriting and applying Chinese traditional construction wisdom.展开更多
文摘OBJECTIVE: To describe a case of Ehlers-Danlos syndrome type IV and its pedigree in China. METHODS: Clinical materials of a case of Ehlers-Danlos syndrome type IV and a pedigree of 6 members within 4 generations were analyzed. Dilated internal jugular vein in the proband was removed by operation. The diagnosis, surgical treatment, and postoperative complications were retrospectively reviewed. RESULTS: Vessels of the proband in the pedigree were crisp and easily lacinated during the procedure of removing his internal jugular vein. Repeating postoperative hematomas were found though complete stanching was achieved during the operation. The patient was successfully recovered by promptly debridgement and needle sucking. The other 5 members of the pedigree all had the triads of Ehlers-Danlos syndrome. CONCLUSIONS: Though it was of extremely low morbidity rate, the high mortality rate and complication of Ehlers-Danlos syndrome deserve great attention during surgical management, especially in patients with Ehlers-Danlos syndrome type IV. Surgeons should be aware of the ponderance of its complications and combined diseases to avoid fatal intraoperative vascular lascination and incontrollable hemorrhage.
基金the National Natural Science Foundation of China(NSFC)Key Program(No.52038007).
文摘Chinese Traditional Maps and Local Chronicles serve as significant sources for investigating the urban history of ancient Chinese cities.These documents prioritize the abstract representation of topological relationships over precise numerical values and geometric shapes.This is consistent with the traditional Chinese city image and spatial schema emphasizing“harmony between man and nature”.Most Chinese Traditional Maps reflect a centripetal spatial schema,wherein the core area is located at the center,and other locations are positioned hierarchically about the center.Based on this data,this research aims to categorize and examine the development and evolution of the centripetal spatial schema in ancient Chinese cities by constructing a pedigree of types.The authors identify three types and summarize their causes,calculate the topological features,and reveal their correlations with the type of pedigree.This study reveals that cities with different centripetal forms exhibit regular differences in the accessibility,centrality,and functional attributes of central nodes,as well as the proportion of nodes with different attributes in the city.Overall,the conclusion aims to deepen people’s understanding of traditional Chinese spatial concepts at the macro-urban level,particularly in the context of China’s current urban renewal wave.Additionally,it provides practical references for inheriting and applying Chinese traditional construction wisdom.
