Introduction: Hypertrophic cardiomyopathy (HCM) belongs to the very heterogeneous group of cardiomyopathies. This study aimed to study myocardial perfusion abnormalities on scintigraphy and assess the risk of sudden d...Introduction: Hypertrophic cardiomyopathy (HCM) belongs to the very heterogeneous group of cardiomyopathies. This study aimed to study myocardial perfusion abnormalities on scintigraphy and assess the risk of sudden death from ventricular arrhythmia in hereditary sarcomeric HCM. Patients and Methods: This is a retrospective and prospective descriptive study over 18 months (January 01, 2021, to July 31, 2022) on the records of patients over 18 with the diagnosis of hypertrophic sarcomeric cardiomyopathy with or without ventricular rhythm disorders and who have undergone myocardial scintigraphy. Results: Three patients were included. The average age of our patients was 66 years old. Dyspnea is the primary symptomatology found in our patients. One patient presented with syncope and unsustained ventricular tachycardia. His risk score for sudden death from ESC at five years is estimated at 6.45%, and the patient received an ICD in primary prevention. The average sudden death risk score of our patients was 3.78%. The mean LV wall thickness was 20 mm. The mean maximum left intraventricular gradient was 39 mmHg. Myocardial fibrosis was present in all our patients. Myocardial scintigraphy was normal in all cases. Conclusion: Hypertrophic cardiomyopathy is a very heterogeneous group of cardiomyopathies. The rhythmic risk is multifactorial and constitutes a significant prognostic factor.展开更多
采用浸渍法制备了 NiO／ZnO－Al2 O3吸附剂，在固定床装置上对模拟焦炉气中的 COS 进行吸附脱除，并采用 XRD 和压汞仪对吸附剂进行了表征。实验结果表明，吸附反应适宜的工艺条件为350℃、0．40 MPa、空速500～1000 h－1，在此条件下...采用浸渍法制备了 NiO／ZnO－Al2 O3吸附剂，在固定床装置上对模拟焦炉气中的 COS 进行吸附脱除，并采用 XRD 和压汞仪对吸附剂进行了表征。实验结果表明，吸附反应适宜的工艺条件为350℃、0．40 MPa、空速500～1000 h－1，在此条件下吸附剂可将焦炉气中的 COS 从320～450 mg／m3降低至0．5 mg／m3，烯烃的体积分数从2．3％～4．5％降为0，其他组分含量不变，吸附剂穿透硫容为17．18％。吸附剂的再生实验表明，吸附剂再生前后晶形、孔结构及硫容变化不大，吸附剂具有较好的再生性能。通过实验总结出脱硫过程为 COS 首先吸附在还原态 Ni 原子上，在 Ni 作用下 COS 中 S－C 断裂生成 NiS，然后生成 H2 S，H2 S 与 ZnO 反应生成 ZnS。展开更多
文摘Introduction: Hypertrophic cardiomyopathy (HCM) belongs to the very heterogeneous group of cardiomyopathies. This study aimed to study myocardial perfusion abnormalities on scintigraphy and assess the risk of sudden death from ventricular arrhythmia in hereditary sarcomeric HCM. Patients and Methods: This is a retrospective and prospective descriptive study over 18 months (January 01, 2021, to July 31, 2022) on the records of patients over 18 with the diagnosis of hypertrophic sarcomeric cardiomyopathy with or without ventricular rhythm disorders and who have undergone myocardial scintigraphy. Results: Three patients were included. The average age of our patients was 66 years old. Dyspnea is the primary symptomatology found in our patients. One patient presented with syncope and unsustained ventricular tachycardia. His risk score for sudden death from ESC at five years is estimated at 6.45%, and the patient received an ICD in primary prevention. The average sudden death risk score of our patients was 3.78%. The mean LV wall thickness was 20 mm. The mean maximum left intraventricular gradient was 39 mmHg. Myocardial fibrosis was present in all our patients. Myocardial scintigraphy was normal in all cases. Conclusion: Hypertrophic cardiomyopathy is a very heterogeneous group of cardiomyopathies. The rhythmic risk is multifactorial and constitutes a significant prognostic factor.
文摘采用浸渍法制备了 NiO／ZnO－Al2 O3吸附剂，在固定床装置上对模拟焦炉气中的 COS 进行吸附脱除，并采用 XRD 和压汞仪对吸附剂进行了表征。实验结果表明，吸附反应适宜的工艺条件为350℃、0．40 MPa、空速500～1000 h－1，在此条件下吸附剂可将焦炉气中的 COS 从320～450 mg／m3降低至0．5 mg／m3，烯烃的体积分数从2．3％～4．5％降为0，其他组分含量不变，吸附剂穿透硫容为17．18％。吸附剂的再生实验表明，吸附剂再生前后晶形、孔结构及硫容变化不大，吸附剂具有较好的再生性能。通过实验总结出脱硫过程为 COS 首先吸附在还原态 Ni 原子上，在 Ni 作用下 COS 中 S－C 断裂生成 NiS，然后生成 H2 S，H2 S 与 ZnO 反应生成 ZnS。
