Split hand/foot malformation (SHFM), formerly known as ectrodactyly is a rare congénital anomaly, its incidence varies from 1/8.500 to 1/25.000 live birth. It mainly affects the development of the limbs, its clin...Split hand/foot malformation (SHFM), formerly known as ectrodactyly is a rare congénital anomaly, its incidence varies from 1/8.500 to 1/25.000 live birth. It mainly affects the development of the limbs, its clinical variability is standard, can present as an isolated feature or as a syndrome associated with other congenital anomalies. Our objective was to present the two cases of SHFM, and to review the literature on the clinical aspects and discuss a probable origin. The father went to school and is a driver because the malformations concerned only the fingers, were less severe, and did not prevent the realization of certain simple gestures of the daily life. On the other hand, the malformations of the fingers of the newborn were severe and the absence of the thumbs compromised the later prehension function. Also the association of a microglossia and a cleft palate contributed to a weight loss that justified hospitalization. The clinical presentation of split hands and feet is variable and the prognosis depends on the type of anomaly. Familial cases suggest a probable genetic origin. Genetic testing is necessary to establish genetic counseling.展开更多
It has been proved by the ancient and modemacupuncture practices that needling techniques are ofvital importance in the acupuncture treatment ofdiseases.At present,much has been reported aboutthe researches on acupunc...It has been proved by the ancient and modemacupuncture practices that needling techniques are ofvital importance in the acupuncture treatment ofdiseases.At present,much has been reported aboutthe researches on acupuncture techniques,which canbe roughly divided into the following three types:reinforcing,reducing,and even methods.Throughlong years of study and clinical practice,Dr.展开更多
In this paper the propagation of elegant Hermite-cosh-Gaussian, elegant Laguerre Gaussian, and Bessel Gaussian beams through a Kerr left-handed metamaterial (LHM) slab have been studied. A split-step Fourier method ...In this paper the propagation of elegant Hermite-cosh-Gaussian, elegant Laguerre Gaussian, and Bessel Gaussian beams through a Kerr left-handed metamaterial (LHM) slab have been studied. A split-step Fourier method is used to investigate the propagation of laser beams through this media. Numerical simulation shows that Gaussian beams have different focusing behaviors in a Kerr LHM slab with positive or negative nonlinearity. Beam focusing happens in slabs with positive nonlinearity and not in slabs with negative nonlinearity; however, negative nonlinearity is required for a Kerr LHM slab to act like a lens. Additionally, the focusing properties of beams can be controlled by controlling the thickness of the slab or the input power of the incident beam. A multilayer structure is also proposed to have beam focusing by thinner slabs and passing longer distances.展开更多
文摘Split hand/foot malformation (SHFM), formerly known as ectrodactyly is a rare congénital anomaly, its incidence varies from 1/8.500 to 1/25.000 live birth. It mainly affects the development of the limbs, its clinical variability is standard, can present as an isolated feature or as a syndrome associated with other congenital anomalies. Our objective was to present the two cases of SHFM, and to review the literature on the clinical aspects and discuss a probable origin. The father went to school and is a driver because the malformations concerned only the fingers, were less severe, and did not prevent the realization of certain simple gestures of the daily life. On the other hand, the malformations of the fingers of the newborn were severe and the absence of the thumbs compromised the later prehension function. Also the association of a microglossia and a cleft palate contributed to a weight loss that justified hospitalization. The clinical presentation of split hands and feet is variable and the prognosis depends on the type of anomaly. Familial cases suggest a probable genetic origin. Genetic testing is necessary to establish genetic counseling.
文摘It has been proved by the ancient and modemacupuncture practices that needling techniques are ofvital importance in the acupuncture treatment ofdiseases.At present,much has been reported aboutthe researches on acupuncture techniques,which canbe roughly divided into the following three types:reinforcing,reducing,and even methods.Throughlong years of study and clinical practice,Dr.
文摘In this paper the propagation of elegant Hermite-cosh-Gaussian, elegant Laguerre Gaussian, and Bessel Gaussian beams through a Kerr left-handed metamaterial (LHM) slab have been studied. A split-step Fourier method is used to investigate the propagation of laser beams through this media. Numerical simulation shows that Gaussian beams have different focusing behaviors in a Kerr LHM slab with positive or negative nonlinearity. Beam focusing happens in slabs with positive nonlinearity and not in slabs with negative nonlinearity; however, negative nonlinearity is required for a Kerr LHM slab to act like a lens. Additionally, the focusing properties of beams can be controlled by controlling the thickness of the slab or the input power of the incident beam. A multilayer structure is also proposed to have beam focusing by thinner slabs and passing longer distances.