Embryologically, chromaffin cells of the pheo-chromocytoma and ganglion cells of the ganglioneuroma are both derived from neural crest cells. Composite pheochromocytoma-ganglioneuroma (Pheo-GN) in a single adrenal gla...Embryologically, chromaffin cells of the pheo-chromocytoma and ganglion cells of the ganglioneuroma are both derived from neural crest cells. Composite pheochromocytoma-ganglioneuroma (Pheo-GN) in a single adrenal gland is very rare. A case report of a patient with composite Pheo-GN of the adrenal gland and renal pelvic cancer is presented. Laparoscopic left adrenalectomy, nephroureterectomy and para-aortic lymphadenectomy were performed. This represents the first report of simultaneous surgical treatment for composite Pheo-GN and renal pelvic cancer.展开更多
Paragangliomas are extra-adrenal pheochromocytomas that derive from chromaffin cells and arise along the sympathetic paraganglia in the body.In the majority of cases,they are secretory tumors and most commonly present...Paragangliomas are extra-adrenal pheochromocytomas that derive from chromaffin cells and arise along the sympathetic paraganglia in the body.In the majority of cases,they are secretory tumors and most commonly present with palpitations.Plasma metanephrines are the standard screening tests for making the diagnosis which is confirmed by pathology.Imaging plays a very important role in establishing the diagnosis.However,there is no specific feature on imaging for paragangliomas;the vascularity of the tumor should show as hyper-enhancing lesions but this is not always the case.The diagnostic value of PET is yet a matter of debate.We present a very rare case of a paraganglioma arising at the renal hilum,splaying the renal artery and vein and causing vascular compromise to the left kidney.The patient presented with an atypical presentation of unrelenting fever that was followed by acute colicky pain.Based on imaging and blood metanephrine levels,the diagnosis of paraganglioma was made.Resection of the tumor was achieved and the patient is now asymptomatic.展开更多
INTRODUCTION Pheochromocytoma is a rare catecholamine-producing tumor with the primary presentations, both of intermittent fever and nonoliguric acute renal failure. Only several articles were retrieved with the rare ...INTRODUCTION Pheochromocytoma is a rare catecholamine-producing tumor with the primary presentations, both of intermittent fever and nonoliguric acute renal failure. Only several articles were retrieved with the rare presentation of fever. However, no case characterized by both of fever and acute renal failure has been retrieved.展开更多
文摘Embryologically, chromaffin cells of the pheo-chromocytoma and ganglion cells of the ganglioneuroma are both derived from neural crest cells. Composite pheochromocytoma-ganglioneuroma (Pheo-GN) in a single adrenal gland is very rare. A case report of a patient with composite Pheo-GN of the adrenal gland and renal pelvic cancer is presented. Laparoscopic left adrenalectomy, nephroureterectomy and para-aortic lymphadenectomy were performed. This represents the first report of simultaneous surgical treatment for composite Pheo-GN and renal pelvic cancer.
文摘Paragangliomas are extra-adrenal pheochromocytomas that derive from chromaffin cells and arise along the sympathetic paraganglia in the body.In the majority of cases,they are secretory tumors and most commonly present with palpitations.Plasma metanephrines are the standard screening tests for making the diagnosis which is confirmed by pathology.Imaging plays a very important role in establishing the diagnosis.However,there is no specific feature on imaging for paragangliomas;the vascularity of the tumor should show as hyper-enhancing lesions but this is not always the case.The diagnostic value of PET is yet a matter of debate.We present a very rare case of a paraganglioma arising at the renal hilum,splaying the renal artery and vein and causing vascular compromise to the left kidney.The patient presented with an atypical presentation of unrelenting fever that was followed by acute colicky pain.Based on imaging and blood metanephrine levels,the diagnosis of paraganglioma was made.Resection of the tumor was achieved and the patient is now asymptomatic.
文摘INTRODUCTION Pheochromocytoma is a rare catecholamine-producing tumor with the primary presentations, both of intermittent fever and nonoliguric acute renal failure. Only several articles were retrieved with the rare presentation of fever. However, no case characterized by both of fever and acute renal failure has been retrieved.
