Purpose: To report the optical coherence tomographic (OCT)- findings in a case of Best’ s disease. Design: Observational case report. Methods: Optical coherence tomography was carried out to understand the pathogenes...Purpose: To report the optical coherence tomographic (OCT)- findings in a case of Best’ s disease. Design: Observational case report. Methods: Optical coherence tomography was carried out to understand the pathogenesis of Best’ s disease in a 13- year- old girl. Results: Optical coherence tomography demonstrated that the lipofuscin accumulated in a cystic space underneath the retinal pigment epithelium in the “ pseudohypopyon stage” of Best’ s disease. It also demonstrated the disruption of the photoreceptors in the “ scrambled egg” stage. Conclusions: These new OCT findings could explain the retention of good visual acuity in the “ pseudohypopyon stage” and the loss of visual acuity in the “ scrambled egg” stage of Best’ s disease.展开更多
文摘Purpose: To report the optical coherence tomographic (OCT)- findings in a case of Best’ s disease. Design: Observational case report. Methods: Optical coherence tomography was carried out to understand the pathogenesis of Best’ s disease in a 13- year- old girl. Results: Optical coherence tomography demonstrated that the lipofuscin accumulated in a cystic space underneath the retinal pigment epithelium in the “ pseudohypopyon stage” of Best’ s disease. It also demonstrated the disruption of the photoreceptors in the “ scrambled egg” stage. Conclusions: These new OCT findings could explain the retention of good visual acuity in the “ pseudohypopyon stage” and the loss of visual acuity in the “ scrambled egg” stage of Best’ s disease.
